伴有跳跃区（节段性无神经节症）的先天性巨结肠病
Hirschsprung's disease with skip area (segmental aganglionosis).
作者信息
Martin L W, Buchino J J, LeCoultre C, Ballard E T, Neblett W W
出版信息
J Pediatr Surg. 1979 Dec;14(6):686-7. doi: 10.1016/s0022-3468(79)80245-6.
PMID:551144
Abstract
Hirschsprung's disease is characterized by a single aganglionic segment of colon extending distally to the anal margin. Well documented reports of segmental aganglionosis have been rare. We report a case of segmental aganglionosis in which there were two distinct aganglionic segments resected. The entire transverse colon between the two aganglionic segments was normally ganglionated, preserved, and utilized and functions in a normal fashion.
摘要
先天性巨结肠症的特征是单个无神经节的结肠段向肛门边缘远端延伸。关于节段性无神经节症的充分记录报告很少见。我们报告一例节段性无神经节症病例，其中切除了两个不同的无神经节段。两个无神经节段之间的整个横结肠神经节正常，得以保留并正常发挥功能。
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