Unal D, Camboulives J, Chapoy P, Viard L, Deguara L M
Anesth Analg (Paris). 1979;36(11-12):517-24.
Two cases of Reye's syndrome aged 11 and 13 are reported, confirmed by hepatic biopsy. The favorable outcome observed in the second case seems to be more related with supportive therapy than exsanguinotransfusion and peritoneal dialysis. The physiopathology of this syndrome is not quite clear, but probably in relation with a diffuse mitochondrial insult. Early diagnosis and supportive therapy are important for a favorable outcome.
报告了两例分别为11岁和13岁的瑞氏综合征病例,经肝活检确诊。第二例观察到的良好预后似乎更多与支持性治疗有关,而非放血输血和腹膜透析。该综合征的病理生理学尚不完全清楚,但可能与弥漫性线粒体损伤有关。早期诊断和支持性治疗对于取得良好预后很重要。