Kaftandziev D, Saradnici I
Acta Chir Iugosl. 1977;24(2):177-83.
The authors presented a rare case with localised congenital supravalvular aortic stenosis associated with bicuspid aortic valvular stenosis which has been surgically treated. The clinical diagnosis was suggested in the presented patient by typical "elfin" face and conformed by left cardiac catheterisation and angiography. The operative procedure with cardiopulmonary by pass consisted of longitudinal aortotomy and insertion of Dacron prosthesis. In addition "open" commissurotomy of partially fused commissures of the bicuspid aortic valve was done. This effectively released the obstruction and enlarged the orifice. The postoperative course was uneventful.
作者报告了一例罕见的局限性先天性主动脉瓣上狭窄合并二叶式主动脉瓣狭窄的病例，并对其进行了手术治疗。该患者因典型的“小精灵”面容提示临床诊断，经左心导管检查和血管造影得以证实。在体外循环下进行的手术操作包括纵行主动脉切开术和植入涤纶人工血管。此外，还对二叶式主动脉瓣部分融合的瓣叶进行了“开放”式交界切开术。这有效地解除了梗阻并扩大了瓣口。术后过程顺利。
