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A case of juvenile lipidosis: electron microscopic, histochemical and biochemical studies.

作者信息

Suzuki K, Johnson A B, Marquet E, Suzuki K

出版信息

Acta Neuropathol. 1968 Sep 2;11(2):122-39. doi: 10.1007/BF00690216.

DOI:10.1007/BF00690216
PMID:5697603
Abstract
摘要

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本文引用的文献

1
THE FINE STRUCTURE OF LIPOFUSCIN AGE PIGMENT IN THE NERVOUS SYSTEM OF AGED MICE.衰老鼠神经细胞系统中脂褐素色素的细微结构。
J Cell Biol. 1965 Sep 1;26(3):779-95. doi: 10.1083/jcb.26.3.779.
2
A study of fixation for electron microscopy.电子显微镜固定研究。
J Exp Med. 1952 Mar;95(3):285-98. doi: 10.1084/jem.95.3.285.
3
Brain ceramide hexosides in Tay-Sachs disease and generalized gangliosidosis (GM1-gangliosidosis).泰-萨克斯病和全身性神经节苷脂贮积症(GM1-神经节苷脂贮积症)中的脑神经酰胺己糖苷。
伴有镶边空泡的远端肌病活检肌肉中的管状膜样和指纹样包涵体。
Acta Neuropathol. 1984;62(3):194-200. doi: 10.1007/BF00691852.
4
Accumulation of smooth cisterns, multivesicular bodies and "zebra" bodies in neurons. A case of peculiar storage condition.神经元中平滑池、多囊泡体和“斑马”体的蓄积。一例特殊的储存状态病例。
Acta Neuropathol. 1971;18(2):132-43. doi: 10.1007/BF00687601.
5
Electron microscopic study on a case of idiocy: astrocytes and mental deficiency.
Acta Neuropathol. 1970;16(1):25-34. doi: 10.1007/BF00686960.
6
[The ultrastructure of protagon (pi) granules].[主角(π)颗粒的超微结构]
Acta Neuropathol. 1970;15(1):56-69. doi: 10.1007/BF00690689.
7
Additional electron microscopic observations on two cases of Batten-Spielmeyer-Vogt disease. (Neuronal ceroid-lipofuscinosis).关于两例巴滕-施皮尔曼-沃格特病(神经元蜡样脂褐质沉积症)的额外电子显微镜观察结果。
Acta Neuropathol. 1971;17(2):85-102. doi: 10.1007/BF00687485.
8
The effect of aging on lysosomal permeability in nerve cells of the central nervous system. An enzyme histochemical study in rat.衰老对中枢神经系统神经细胞溶酶体通透性的影响。大鼠的酶组织化学研究。
Histochemie. 1972;30(4):315-24. doi: 10.1007/BF00279780.
9
The electron microscopic study of the appendix as early diagnostic means in Batten-Spielmeyer-Vogt disease.
Acta Neuropathol. 1972;21(2):169-75. doi: 10.1007/BF00687571.
10
[Pigment variant of the adult type of amaurotic idiocy (Kufs) (author's transl)].成人型黑蒙性白痴(库夫斯病)的色素变异型(作者译)
Acta Neuropathol. 1973 Nov 5;26(3):225-36. doi: 10.1007/BF00684432.
J Lipid Res. 1967 Mar;8(2):105-13.
4
Oxidative histochemistry of reactive astrocytes.反应性星形胶质细胞的氧化组织化学
Arch Neurol. 1962 Sep;7:211-8. doi: 10.1001/archneur.1962.04210030049007.
5
ULTRASTRUCTURAL AND BIOCHEMICAL OBSERVATIONS ON A CASE OF SYSTEMIC LATE INFANTILE LIPIDOSIS AND ITS RELATIONSHIP TO TAY-SACHS DISEASE AND GARGOYLISM.一例全身性晚发性婴儿脂质沉积症的超微结构及生化观察及其与泰-萨克斯病和黏多糖贮积症的关系
J Neuropathol Exp Neurol. 1965 Apr;24:318-40. doi: 10.1097/00005072-196504000-00011.
6
GENERALIZED GANGLIOSIDOSIS: ANOTHER INBORN ERROR OF GANGLIOSIDE METABOLISM?全身性神经节苷脂沉积症:另一种神经节苷脂代谢的先天性缺陷?
Am J Dis Child. 1965 Apr;109:338-46.
7
FINE STRUCTURE OF THE LIPID BODIES IN JUVENILE AMAUROTIC IDIOCY.少年型黑蒙性白痴中脂质小体的精细结构
Acta Neuropathol. 1963 Nov 5;3:144-9. doi: 10.1007/BF00687063.
8
ON THE NATURE OF THE "STORED" LIPID SUBSTANCES IN JUVENILE AMAUROTIC IDIOCY (BATTEN-SPIELMEYER-VOGT).关于青少年黑蒙性白痴(巴滕 - 施皮尔迈尔 - 沃格特病)中“储存”脂质物质的性质
Ann Histochim. 1963 Jul-Sep;8:255-7.
9
A CASE OF JUVENILE LIPIDOSIS: THE SIGNIFICANCE OF ELECTRON MICROSCOPIC AND BIOCHEMICAL OBSERVATIONS OF A CEREBRAL BIOPSY.一例青少年脂质沉积症:脑活检的电子显微镜和生化观察的意义
J Neuropathol Exp Neurol. 1963 Oct;22:557-80.
10
CHROMATOGRAPHIC SEPARATION OF HUMAN BRAIN GANGLIOSIDES.人脑海藻糖神经节苷脂的色谱分离
J Neurochem. 1963 Sep;10:613-23. doi: 10.1111/j.1471-4159.1963.tb08933.x.