Hadchouel M, Hugon R N, Gautier M
Arch Pathol Lab Med. 1978 Aug;102(8):402.
The syndrome of "paucity" of intrahepatic bile ducts is characterized by a reduction of the ratio of interlobular bile ducts to portal areas. The present unidirectional study of liver biopsy specimens in cases of so-called intrahepatic biliary atresia, controlled essentially by age-matched autopsy control, showed that there is also a reduced number of portal areas in the livers of these subjects. This fact suggests an injury to the vascular anlage associated with biliary injury.
肝内胆管“稀少”综合征的特征是小叶间胆管与门静脉区域的比例降低。目前对所谓肝内胆管闭锁病例的肝活检标本进行的单向研究，基本上以年龄匹配的尸检对照为依据，结果显示这些受试者肝脏中的门静脉区域数量也减少。这一事实表明与胆管损伤相关的血管原基受到了损伤。
