杜氏肌营养不良症的进一步运动单位研究。
Further motor unit studies in Duchenne muscular dystrophy.
作者信息
McComas A J, Sica R E, Brandstater M E
出版信息
J Neurol Neurosurg Psychiatry. 1977 Dec;40(12):1147-51. doi: 10.1136/jnnp.40.12.1147.
Abstract
Numbers of functioning motor units have been estimated in 124 muscles of boys with Duchenne dystrophy; some of the patients were studied on several occasions. In the distal muscles examined (extensor digitorum brevis, thenar, and hypothenar muscles) the losses of units were probably present at birth and did not decrease with age. In contrast, the numbers of units and of excitable muscle fibres in the soleus muscles declined significantly, especially between the ages of 9 and 12 years.
摘要
已经对患有杜氏肌营养不良症男孩的124块肌肉中的功能性运动单位数量进行了估计；部分患者接受了多次研究。在所检查的远端肌肉（趾短伸肌、大鱼际肌和小鱼际肌）中，运动单位的损失可能在出生时就已存在，并且不会随着年龄增长而减少。相比之下，比目鱼肌中的运动单位数量和可兴奋肌纤维数量显著下降，尤其是在9至12岁之间。
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