Abraham F A, Cohen D, Sohmer H
Doc Ophthalmol. 1977 Dec 30;44(2):435-44. doi: 10.1007/BF00230092.
The symptoms of Usher's syndrome - congenital hearing impairment and tapetoretinal dystrophy - are difficult to detect in young children. The electroretinogram (ERG), visual evoked potential (VEP), auditory nerve and brain-stem responses as well as the cochlear microphonic potentials were used to evaluate the defects of the visual and auditory systems in 20 patients, 3-45 years of age. This study demonstrates the usefulness, reliability and convenience of the electrophysiological tests for early diagnosis and functional evaluation of Usher's syndrome.
尤塞氏综合征的症状——先天性听力障碍和视网膜色素变性——在幼儿中很难被察觉。我们使用视网膜电图（ERG）、视觉诱发电位（VEP）、听神经和脑干反应以及耳蜗微音器电位，对20名年龄在3至45岁之间的患者的视觉和听觉系统缺陷进行了评估。这项研究证明了电生理测试在尤塞氏综合征早期诊断和功能评估中的实用性、可靠性和便利性。
