Godeau P, Bletry O, Teillac D, Herreman G, Wechsler B
Nouv Presse Med. 1977 Dec 17;6(43):4039-43.
The authors report 8 cases of scleroderma with oedema in the initial stages which could be divided amongst three groups on the basis of their clinical, biological, histological characteristics and course: normal systemic scleroderma, mixed connective tissue disease, Shulmans syndrome. The relationship between one of these cases and Buschke's scleroderma is discussed. These cases of scleroderma are characterized by diagnostic difficulties in the initial phase and by their relatively favourable vital prognosis (one death only). Corticosteroids may be effective to some extent in the presence of mixed connective tissue disease of Shulman's syndrome.
作者报告了8例硬皮病初期伴有水肿的病例，根据其临床、生物学、组织学特征及病程可分为三组：系统性硬皮病（病情正常型）、混合性结缔组织病、舒尔曼综合征。文中讨论了其中1例与布施克硬皮病的关系。这些硬皮病病例的特点是初期诊断困难，但生命预后相对良好（仅1例死亡）。在混合性结缔组织病或舒尔曼综合征的情况下，皮质类固醇可能在一定程度上有效。
