一名患有急性间歇性卟啉病的儿童红细胞中原卟啉增加。
Increased protoporphyrin in erythrocytes in a child with acute intermittent porphyria.
作者信息
Gregor A, Kostrzewska E, Prokurat H, Pucek Z, Torbicka E
出版信息
Arch Dis Child. 1977 Dec;52(12):947-50. doi: 10.1136/adc.52.12.947.
Abstract
A child is described with acute intermittent porphyria but having an erythropoietic component, with disordered metabolism of porphyrins in bone marrow.
摘要
描述了一名患有急性间歇性卟啉病但具有红细胞生成成分的儿童，其骨髓中卟啉代谢紊乱。
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PEDIATRIC ASPECTS OF THE PORPHYRIAS.卟啉病的儿科问题
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ISOTOPE STUDIES ON A CASE OF ERYTHROPOIETIC PROTOPORPHYRIA.
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Separation of the coproporphyrin isomers I and III by thin layer chromatography.通过薄层色谱法分离粪卟啉异构体I和III。
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A review of porphyrin metabolism with special reference to childhood.卟啉代谢综述，特别涉及儿童期。
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Porphyrin content of bone marrow and liver in the various forms of porphyria.各种形式卟啉病中骨髓和肝脏的卟啉含量
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Diagnosis and treatment of the porphyrias.卟啉病的诊断与治疗。
Proc R Soc Med. 1968 Feb;61(2):193-6. doi: 10.1177/003591576806100232.
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J Clin Invest. 1971 Jan;50(1):203-7. doi: 10.1172/JCI106474.
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