Matsuki H, Moriya A, Maruyama Y, Ohara S, Babaya K, Hirao Y, Hiramatsu T, Okajima E, Yoshikawa N
Hinyokika Kiyo. 1984 Aug;30(8):1075-84.
Congenital mesoblastic nephroma (CMN) is an unusual renal tumor, similar in some respects to Wilms' tumor and reported only in infants. We report a case of CMN in a 2-year-old boy. He was referred to us with a right abdominal mass. Excretory urogram, arteriogram and computed tomogram revealed a large malignant renal tumor on the right side. With a clinical diagnosis of Wilms' tumor of the right kidney, he received radiation and chemotherapy. After radiation and chemotherapy, tumor size was decreased. Right nephrectomy was performed on April 22, 1982. The kidney and tumor weighed 270 g and measured 12 X 7 X 5 cm. The tumor extended to the renal pelvis and the ureter with polypoid growth pattern. Microscopically, the tumor was composed of compact interlacing bundles of elongated fibromyomatous cells. Islands of entrapped glomeruli and tubules were also detected within the tumor. He was well and had no signs of recurrence of tumor at the age of 3 years.
先天性中胚层肾瘤(CMN)是一种罕见的肾肿瘤,在某些方面与肾母细胞瘤相似,且仅在婴儿中报道。我们报告一例2岁男孩的CMN病例。他因右侧腹部肿块被转诊至我院。排泄性尿路造影、动脉造影和计算机断层扫描显示右侧有一个巨大的恶性肾肿瘤。临床诊断为右肾肾母细胞瘤,他接受了放疗和化疗。放疗和化疗后,肿瘤大小缩小。1982年4月22日进行了右肾切除术。肾脏和肿瘤重270克,大小为12×7×5厘米。肿瘤呈息肉样生长,延伸至肾盂和输尿管。显微镜下,肿瘤由紧密交织的细长纤维肌瘤样细胞束组成。肿瘤内还发现了被困的肾小球和肾小管岛。他3岁时情况良好,没有肿瘤复发的迹象。