Lütschg J
Neuropediatrics. 1984 Sep;15 Suppl:24-7. doi: 10.1055/s-2008-1052378.
The results of nerve conduction velocities, evoked potentials and EEGs in adrenoleukodystrophy, metachromatic leukodystrophy and Pelizaeus Merzbacher's disease are discussed. As shown on the example of four own cases with metachromatic leukodystrophy, the slowing of nerve conduction velocities and the latency prolongation of evoked potentials components or loss of evoked potential components is dependent on the type of MLD (infantile and juvenile) and of the duration of the disease. The pathophysiology of the slowed peripheral and central impulse conduction is discussed.
本文讨论了肾上腺脑白质营养不良、异染性脑白质营养不良和佩利措伊斯-梅茨巴赫病的神经传导速度、诱发电位和脑电图结果。以4例异染性脑白质营养不良患者为例，神经传导速度减慢、诱发电位成分潜伏期延长或诱发电位成分消失取决于异染性脑白质营养不良的类型（婴儿型和青少年型）以及病程。文中还讨论了外周和中枢冲动传导减慢的病理生理学。
