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韦尔默综合征。病例报告。

Wermer's syndrome. A case report.

作者信息

Gray P I, Botha A P, Nel C J, Potgieter G M, Röhm G F, Steyn A F, van den Heever C M

出版信息

S Afr Med J. 1981 Mar 28;59(14):497-8.

PMID:6111132
Abstract

Wermer's syndrome (or multiple endocrine adenomatosis type I) is a hereditary condition characterized by tumours or hyperplasia involving multiple endocrine organs. Most commonly the pituitary and parathyroid glands and the pancreas are involved. We record a further case, the patient presenting with acromegaly due to a pituitary adenoma, hypercalcaemia due to a parathyroid adenoma and peptic ulceration.

摘要

韦默综合征(或Ⅰ型多发性内分泌腺瘤病)是一种遗传性疾病,其特征为多个内分泌器官出现肿瘤或增生。最常受累的是垂体、甲状旁腺和胰腺。我们报告另一例病例,该患者因垂体腺瘤出现肢端肥大症,因甲状旁腺腺瘤出现高钙血症,并伴有消化性溃疡。

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