Friede R L, Schubiger O
J Neurol. 1981;225(1):1-8. doi: 10.1007/BF00313455.
A 62 year-old-man suffered from progressive dementia for the last 5 years of his life. Angiography disclosed draining of multiple extracranial, galeal arteries directly into the superior sagittal sinus with retrograde filling of cerebral veins. At necropsy there was arterialization of the walls of the sinus and a multichannelled lumen in its middle third. The sinus was not distended, the dura normal, and no angioma was found. The leptomeninges and the cerebral white matter contained excessively distended veins, some with thickened fibrotic walls. Many arteries in the arterial white matter were mineralized. There were widespread patches of incomplete demyelination about these abnormal vessels. The lesion was classified as a developmental anomaly with direct shunting of extracranial arteries into the superior sagittal sinus.
一名62岁男性在生命的最后5年患有进行性痴呆。血管造影显示多条颅外颞浅动脉直接引流至上矢状窦，并伴有脑静脉逆行充盈。尸检发现窦壁动脉化，其中段有多个管腔。窦未扩张，硬脑膜正常，未发现血管瘤。软脑膜和脑白质中含有过度扩张的静脉，一些静脉壁增厚纤维化。动脉白质中的许多动脉发生了矿化。在这些异常血管周围有广泛的不完全脱髓鞘斑块。该病变被分类为颅外动脉直接分流至上矢状窦的发育异常。
