Antônio J H, Diniz M C, Miranda D
Cardiology. 1978;63(1):39-46. doi: 10.1159/000169879.
A case of persistent atrial standstill associated with muscular dystrophy of the limb girdle type is reported for the first time in the literature, In spite, of advanced myopathy, the patient delivered an apparently normal child. Hemodynamic studies including a normal coronary cinearteriography were performed in the post-partum period. The patient also had clinical and radiological evidence of peptic ulcer which may be the expression of an excessive vagal tone. A congenitial anomaly of the conduction system might explain the association of left anterior hemiblock with persistent atrial standstill, but could not be demonstrated.
本文首次报道了1例与肢带型肌营养不良相关的持续性心房静止病例。尽管存在晚期肌病,但患者分娩了1个外表正常的婴儿。产后进行了包括正常冠状动脉电影血管造影在内的血流动力学研究。患者还有消化性溃疡的临床和放射学证据,这可能是迷走神经张力过高的表现。传导系统的先天性异常可能解释左前分支阻滞与持续性心房静止的关联,但无法得到证实。