Cabezuelo-Huerta G, Frontera-Izquierdo P, Vázquez-Pérez J
An Esp Pediatr. 1983 Jan;18(1):39-44.
A 1 1/2 year old boy with cyanosis and congestive heart failure was found to have isolated right ventricular hypoplasia with atrial septal defect by cardiac catheterization and angiocardiography. On physical examination no murmur was heard. The ECG revealed a frontal plane AQRS of -45 degrees, right atrial enlargement and left ventricular hypertrophy. Chest X-ray examination showed slight cardiomegaly. Preoperative assessment included temporary occlusion of the atrial septal defect by means of a balloon catheter. Surgical closure of the atrial septal defect was performed at 4 years old. The clinical findings and surgical treatment of this rare malformation are discussed.
一名1岁半患有紫绀和充血性心力衰竭的男孩，经心导管检查和心血管造影发现患有孤立性右心室发育不全合并房间隔缺损。体格检查未闻及杂音。心电图显示额面QRS电轴为 -45度，右心房扩大和左心室肥厚。胸部X线检查显示轻度心脏扩大。术前评估包括通过球囊导管临时封堵房间隔缺损。患儿4岁时进行了房间隔缺损的手术闭合。本文讨论了这种罕见畸形的临床发现和外科治疗。
