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横纹肌肉瘤导致儿童双眼视力迅速丧失。

Rhabdomyosarcoma causing rapid bilateral visual loss in children.

作者信息

Breen L A, Kline L B, Hart W M, Burde R M

出版信息

J Clin Neuroophthalmol. 1984 Sep;4(3):185-8.

PMID:6238056
Abstract

Rhabdomyosarcoma commonly involves the orbit resulting in unilateral proptosis, swelling, and restricted ocular motility. We saw two unusual cases of children with nasopharyngeal rhabdomyosarcoma which caused rapid bilateral visual loss due to simultaneous spread of the tumor to the orbital apices. Initial CT scans revealed the tumor, but were misinterpreted as "normal," causing a significant delay in diagnosis. We recommend high resolution CT scans of the nasopharynx, orbits, and suprasellar region in any child with rapid bilateral visual loss to rule out this common childhood tumor.

摘要

横纹肌肉瘤常累及眼眶,导致单侧眼球突出、肿胀和眼球运动受限。我们见过两例不寻常的儿童鼻咽横纹肌肉瘤病例,肿瘤同时蔓延至眶尖,导致双侧视力迅速丧失。最初的CT扫描显示了肿瘤,但被误诊为“正常”,导致诊断出现显著延误。我们建议,对于任何双侧视力迅速丧失的儿童,都应进行鼻咽、眼眶和鞍上区域的高分辨率CT扫描,以排除这种常见的儿童肿瘤。

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