Godeau P, Bletry O, Zafrani E S, Brion N, Chauveinc L, Galian A
Sem Hop. 1980;56(45-46):1895-900.
Six patients with scleroderma (Barnett's type I and II) associated with hepatopathy are reported. Primary biliary cirrhosis was confirmed in four cases and was probably present in one case, while cirrhosis of unknown origin was present in the sixth patient. The outcome was fatal in two cases. Salivary secretions were reduced in all six cases, and a diagnosis of Gougerot-Sjögren's disease was confirmed in four patients. The frequency with which this triple association has been reported suggests that its incidence has been underestimated.
报告了6例硬皮病(巴尼特I型和II型)合并肝病的患者。4例确诊为原发性胆汁性肝硬化,1例可能患有该病,而第6例患者为不明原因的肝硬化。2例患者预后不良。所有6例患者唾液分泌均减少,4例患者确诊为古热罗-舍格伦病。已有报道这种三联征的发生频率,提示其发病率可能被低估。