Landau J F, Batisse A, Fermont L, Piechaud J F, Kachaner J
Sem Hop. 1982 Jan 14;58(2):93-7.
All cardiovascular malformations compromise ventricular function and lead to alterations in the myocardial structure. Most of these are adaptive reactions. However, in some cases, this reaction overreaches its object and leads to an authentic myocardiopathy. This myocardiopathy is usually hypertrophic in obstacles which result in systolic overload of the left ventricle (coarctation peri-orificial stenosis of the aorta, systemic hypertension) or of the right ventricle (pulmonic stenosis), or congestive in diastolic overload by left-to-right shunts or valvular insufficiency. These myocardiopathies may prevent recognition of the signs of the underlying heart disease thereby leading to diagnostic errors and delay in therapy. They may constitute the main factor of an operative decision.
所有心血管畸形都会损害心室功能，并导致心肌结构改变。其中大多数是适应性反应。然而，在某些情况下，这种反应会过度，导致真正的心肌病。这种心肌病在导致左心室收缩期负荷过重（主动脉缩窄、主动脉瓣周狭窄、系统性高血压）或右心室收缩期负荷过重（肺动脉狭窄）的梗阻性病变中通常表现为肥厚型，而在由左向右分流或瓣膜关闭不全导致舒张期负荷过重的病变中则表现为充血型。这些心肌病可能会妨碍对潜在心脏病体征的识别，从而导致诊断错误和治疗延误。它们可能构成手术决策的主要因素。
