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一名患有冯·雷克林霍增氏神经纤维瘤病的患者猝死。

Sudden death in a patient with Von Recklinghausen's neurofibromatosis.

作者信息

Unger P D, Taff M L, Song S, Schwartz I S

出版信息

Am J Forensic Med Pathol. 1984 Jun;5(2):175-9. doi: 10.1097/00000433-198406000-00014.

Abstract

Sudden death caused by tumors is uncommon. Death attributable to an unsuspected primary intracranial neoplasm is especially rare. An undiagnosed brain tumor is particularly unusual in a patient with Von Recklinghausen's neurofibromatosis (NF). A young man with known NF, with no manifest central nervous system involvement, died less than 24 hours after plastic surgery. A glioblastoma multiforme was discovered at autopsy.

摘要

肿瘤导致的猝死并不常见。由未被怀疑的原发性颅内肿瘤引起的死亡尤其罕见。未被诊断出的脑肿瘤在患有冯·雷克林霍增氏神经纤维瘤病(NF)的患者中尤为不寻常。一名患有已知NF且无明显中枢神经系统受累的年轻人,在接受整形手术后不到24小时死亡。尸检时发现了多形性胶质母细胞瘤。

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