Sangüeza P, Jove N
Med Cutan Ibero Lat Am. 1983;11(5):307-10.
We present two cases of recurrent digital fibromatosis, one of them presented lesions since birth, aun the other one since seven months of age. The first case was treated surgically, with relapses and marked deformities. The second one underwent only biopsy. Histopathologic examination showed active fibroblasts, in whorl disposition, and intracytoplasmic inclusions in both cases. By its natural evolution, we believe that recurrent infantile digital fibromatosis has an initial stage, a tumoral or hyperplastic stage, and finally spontaneous evolution, which explains the fact that it is not found in adults.
我们报告两例复发性指纤维瘤病,其中一例自出生就出现病变,另一例自七个月大时出现。第一例接受了手术治疗,但复发且出现明显畸形。第二例仅进行了活检。组织病理学检查显示,两例均有呈漩涡状排列的活跃成纤维细胞及胞质内包涵体。就其自然病程而言,我们认为复发性婴儿指纤维瘤病有一个初始阶段、一个肿瘤或增生阶段,最终会自发演变,这解释了为何在成年人中未发现该病。