Avagnina A, Elsner B, De Marco L, Bracco A N, Nazar J, Pavlovsky H
Cancer. 1984 May 1;53(9):1948-51. doi: 10.1002/1097-0142(19840501)53:9<1948::aid-cncr2820530924>3.0.co;2-j.
A unique case of pulmonary rhabdomyosarcoma with an isolated, symptomatic small bowel metastasis is presented. The tumor affected the middle lobe, and was treated with a right pneumonectomy. Eleven months after the operation, an isolated small bowel metastasis, which produced intestinal obstruction, was resected. The patient is currently alive, 11 months after operation. The myogenous nature of the tumor was confirmed by the immunohistochemical demonstration of myoglobin in the pulmonary and enteric lesion by the ultrastructural findings of poorly developed sarcomeres.
本文报告一例独特的肺横纹肌肉瘤病例，该病例伴有孤立的、有症状的小肠转移。肿瘤累及中叶，接受了右肺切除术。术后11个月，切除了导致肠梗阻的孤立小肠转移灶。患者目前在术后11个月仍存活。通过肺和肠道病变中肌红蛋白的免疫组化证实以及发育不良的肌节的超微结构发现，确诊了肿瘤的肌源性本质。
