Fukushima N, Matsuura N, Nohara Y, Fujita H, Endo M, Abe K, Kosaka S, Satomi S
Tohoku J Exp Med. 1984 Oct;144(2):129-38. doi: 10.1620/tjem.144.129.
We described here a 12-year-old male patient with the syndrome of insulin resistance and acanthosis nigricans type A. Insulin levels at fasting state and after glucose loading were 149 +/- 63 microU/ml (mean +/- S.D.) and over 1,000 microU/ml respectively, while the fasting level of blood glucose was 77.7 +/- 8.9 mg/ml (mean +/- S.D.). A marked resistance to exogenous insulin was observed. Circulating levels of insulin antagonists such as growth hormone, cortisol and glucagon were within the normal range. Proinsulin was less than 5% of the radioimmunoassayable insulin. No insulin antibody or antireceptor antibody was detected. Insulin binding to mononuclear cells was decreased to about 50% of the controls. Analysis of membrane receptors demonstrated the normal average affinity, dissociation kinetics and negative cooperativity with a decreased number of receptors. After two days fasting, plasma IRI levels decreased to 27 microU/ml, while insulin binding kinetics were not affected; which suggests that the receptor decrease was not secondary to hyperinsulinemia. These findings indicate that the decreased number of receptors was one of the causes for insulin resistance in this patient.
我们在此描述了一名患有A型胰岛素抵抗和黑棘皮病综合征的12岁男性患者。空腹状态及葡萄糖负荷后胰岛素水平分别为149±63微单位/毫升(均值±标准差)和超过1000微单位/毫升,而空腹血糖水平为77.7±8.9毫克/毫升(均值±标准差)。观察到对外源性胰岛素有明显抵抗。胰岛素拮抗剂如生长激素、皮质醇和胰高血糖素的循环水平在正常范围内。胰岛素原占可放射免疫测定胰岛素的比例小于5%。未检测到胰岛素抗体或抗受体抗体。胰岛素与单核细胞的结合减少至对照的约50%。膜受体分析显示平均亲和力、解离动力学正常且具有负协同性,但受体数量减少。禁食两天后,血浆胰岛素免疫反应性(IRI)水平降至27微单位/毫升,而胰岛素结合动力学未受影响;这表明受体减少并非继发于高胰岛素血症。这些发现表明受体数量减少是该患者胰岛素抵抗的原因之一。