Dewilde J, Bellorini M, Signoret P, Vahanian A, Bourroux A, Cachera J P, Acar J, Gamerman J
Arch Mal Coeur Vaiss. 1983 Jan;76(1):113-8.
The echocardiographic appearances of a patient with a rare congenital malformation, interatrial septal aneurysm (IASA) associated with a hemodynamically significant left-to-right shunt, are described. A 52 year old man with Noonan's syndrome was admitted to hospital for atrial flutter with right heart failure, which, on investigation, led to the diagnosis of a rare type of atrial septal defect; 2D echocardiography showed an isolated aneurysm of the interatrial septum; cardiac catheterisation demonstrated a significant left-to-right (5 volumes of oxygen per 100 ml). The patient underwent surgery which confirmed the presence of a multiperforated aneurysm of the interatrial septum in the region of the fossa ovalis. This abnormality was resected and the interatrial defect closed; there were no postoperative complications and the cardiomegaly regressed significantly. The authors underline the M mode and 2D appearances of this condition; although it may be difficult on M mode examination to distinguish an IASA from other conditions giving rise to mobile intra-right atrial echos, such as Chiari's malformation, tricuspid valve vegetations, intraatrial tumour or thrombus or Eustachian valve, 2D examination using different incidences and contrast injections generally confirms the diagnosis. Surgery is often necessary after the detection of this echocardiographic abnormality: the surgical indications are described.
本文描述了一名患有罕见先天性畸形——房间隔瘤(IASA)并伴有具有血流动力学意义的左向右分流的患者的超声心动图表现。一名患有努南综合征的52岁男性因心房扑动伴右心衰竭入院,经检查诊断为一种罕见类型的房间隔缺损;二维超声心动图显示房间隔孤立性瘤样膨出;心导管检查显示存在明显的左向右分流(每100ml血液中有5个氧容量)。患者接受了手术,术中证实卵圆窝区域存在多孔性房间隔瘤。切除该异常结构并闭合房间隔缺损;术后无并发症,心脏扩大明显减轻。作者强调了这种情况的M型和二维表现;尽管在M型检查中可能难以将IASA与其他导致右房内活动回声的情况区分开来,如 Chiari 畸形、三尖瓣赘生物、心房肿瘤或血栓或欧氏瓣,但使用不同入射角和造影剂注射的二维检查通常可确诊。在检测到这种超声心动图异常后通常需要进行手术:文中描述了手术指征。