Multiple meningiomas of the cervical spinal cord associated with Klippel-Feil malformation and atlantooccipital assimilation.

A case of multiple meningiomas confined solely to the cervical spinal canal in association with multiple bony abnormalities of the cervical spine is presented. The relationship of this entity to neurofibromatosis, whether the central type or a form fruste, is explored. It is suggested that multiple meningiomas unassociated with other central or peripheral tumors may present a distinct clinical entity and may occur in an as yet uncharacterized familial pattern.