Schoos-Barbette S, Gerard J, Francotte N, Lambotte C
J Inherit Metab Dis. 1984;7(4):165-7. doi: 10.1007/BF01805601.
The treatment comprising a special diet (without glycine, serine, and with a reduced amount of threonine), strychnine nitrate and ursodesoxycholic acid (UDCA) led to normoglycinaemia in this form of severe non-ketotic glycine encephalopathy. Diet and treatment were well tolerated but without significant effect upon psychomotor development. This treatment should be more effective if administered before irreversible brain damage occurs, particularly in moderate and chronic forms of NKH.
这种治疗方法包括特殊饮食（不含甘氨酸、丝氨酸，苏氨酸含量减少）、硝酸士的宁和熊去氧胆酸（UDCA），在这种严重的非酮症甘氨酸脑病形式中可导致正常甘氨酸血症。饮食和治疗耐受性良好，但对精神运动发育没有显著影响。如果在不可逆的脑损伤发生之前进行治疗，尤其是在中度和慢性NKH形式中，这种治疗应该会更有效。
