Liew S H, Haynes M
Pathology. 1981 Apr;13(2):257-66. doi: 10.3109/00313028109081665.
Three cases of the localized form of congenital generalized fibromatosis are described in females under one year. The lesions were in the parotid region, biceps muscle and abdominal wall. The infiltrative or nodular pattern of these tumours with the periphery resembling smooth muscle and the central portion resembling a haemangiopericytoma makes them a distinct histological entity. Ultrastructurally, these tumours are composed of myofibroblasts. The differential diagnosis from other soft tissue tumours in infancy and early childhood is discussed. These tumours are benign and recurrence after complete local excision is rare.
本文描述了3例1岁以下女性先天性全身性纤维瘤病的局限性病例。病变位于腮腺区、肱二头肌和腹壁。这些肿瘤的浸润性或结节性形态，周边类似平滑肌，中央部分类似血管外皮细胞瘤，使其成为一种独特的组织学实体。超微结构上，这些肿瘤由肌成纤维细胞组成。文中讨论了与婴幼儿期其他软组织肿瘤的鉴别诊断。这些肿瘤为良性，完整局部切除后很少复发。
