Quero Jiménez C, Cazzaniga M, Quero Jiménez M, Paves Sanz M, Pena I, Barrios M C
An Esp Pediatr. 1981 Jan;14(1):7-18.
Diagnostic features of the absent pulmonary valve syndrome are reported. Association of this syndrome with ventricular septal defect, tetralogy of Fallot and tricuspid atresia is stressed. Severe ventilatory problems are frequent during the neonatal period. A exaggerated right ventricular hypertrophy, in comparison with that expected in the usual case of tetralogy of Fallot, is a useful parison with that expected in the usual case of tetralogy of Fallot, is a useful electrocardiographic sign. Complete diagnosis sometimes requires the technique of occlusion aortography sign. Complete diagnosis sometimes requires the technique of occlusion aortography or contrast injections into pulmonary veins.
报道了肺动脉瓣缺如综合征的诊断特征。强调了该综合征与室间隔缺损、法洛四联症和三尖瓣闭锁的关联。新生儿期常出现严重的通气问题。与法洛四联症常见病例相比，右心室肥厚过度，这是一个有用的心电图征象。完整的诊断有时需要采用主动脉造影阻塞技术或向肺静脉注射造影剂。
