Herzberg J
Z Hautkr. 1981 Oct 15;56(20):1317-25.
5 new patients with REM-Syndromes are reported; 4 of them are completely consistent with the first description of Steigleder, Gartmann and Linker. The 5th patient reveals some special clinical and histochemical signs, but also belongs to the REM-syndrome. All cases are different from the plaque-like form of cutaneous mucinosis of Perry et al. (A typical case of this condition was also seen by the author, but is not included in this study). The absence of symptoms, the resistance against any therapy with the exception of synthethic antimalarials, the characteristic localisation and the stereotype clinical signs, the characteristic histochemical findings are remarkable. Even in the HE-stain the histological pattern suggests the diagnosis of REM-syndrome.
报告了5例快速眼动睡眠行为障碍(REM-Syndromes)新患者;其中4例与施泰格勒德、加特曼和林克的首次描述完全一致。第5例患者表现出一些特殊的临床和组织化学特征,但也属于快速眼动睡眠行为障碍。所有病例均与佩里等人的斑块状皮肤粘蛋白病不同。(作者也见过这种情况的一个典型病例,但未纳入本研究)。无症状、除合成抗疟药外对任何治疗均有抵抗、特征性定位和刻板的临床体征、特征性组织化学发现都很显著。即使在苏木精-伊红(HE)染色中,组织学模式也提示快速眼动睡眠行为障碍的诊断。