Otero Coto E, Quero Jimenez M, Deverall P B, Bain H
Pediatr Cardiol. 1984 Jan-Mar;5(1):1-5. doi: 10.1007/BF02306740.
Seven specimens with a 'cleft' mitral valve associated with anomalous chordal fixation and abnormal ventriculo-arterial connection are presented. Four were associated with a discordant ventriculo-arterial connection, two with double-outlet right ventricle, and one with double-outlet left ventricle. In six the chordae from the cleft were attached to the anterior border of a small ventricular septal defect. In the seventh the chordae were attached to an accessory papillary muscle in the left ventricular outflow tract. These clefts differ from those of atrioventricular defects. The cleft is more anterior, there are no septal defects of the atrioventricular canal type, and no deficiency of the basal ventricular septum. Mitral regurgitation or left ventricular outlet obstruction are possible consequences of the anomaly.
本文报告了7例伴有异常腱索固定和心室-动脉连接异常的“裂缺”二尖瓣标本。其中4例伴有心室-动脉连接不一致，2例伴有右心室双出口，1例伴有左心室双出口。6例中，裂缺处的腱索附着于小室间隔缺损的前缘。第7例中，腱索附着于左心室流出道的一个副乳头肌上。这些裂缺与房室缺损的裂缺不同。该裂缺更靠前，没有房室管型的间隔缺损，也没有心室基底部间隔的缺损。二尖瓣反流或左心室流出道梗阻可能是该异常的后果。
