Babiker M A, El Seed F A
Scand J Haematol. 1984 Jul;33(1):54-8. doi: 10.1111/j.1600-0609.1984.tb02210.x.
The rare combination of sickle cell trait with hereditary spherocytosis in a Sudanese family is reported. The splenic hypofunction and fibrosis as a result of sickling has ameliorated the clinical course of the 35 year old father. The symptoms of a six years old son seem to be getting milder with age too. The family is managed conservatively and splenectomy was not required.
据报道,在一个苏丹家庭中出现了镰状细胞性状与遗传性球形红细胞增多症的罕见组合。镰状化导致的脾功能减退和纤维化改善了这位35岁父亲的临床病程。一名6岁儿子的症状似乎也随着年龄增长而减轻。该家庭采用保守治疗,无需进行脾切除术。