Lammer J, Fotter R, Becker H
Eur J Radiol. 1984 Aug;4(3):198-201.
Congenital bile duct dilatation is an autosomal recessive inherited disease. Pathologically tortuous dilated, dysplastic intrahepatic bile ducts were found. It may be associated with hepatic fibrosis (Grumbach's disease), or without (Caroli's disease). A common additional finding is an infantile polycystic kidney. Three cases are reported and the radiological and sonographic findings are discussed.
先天性胆管扩张是一种常染色体隐性遗传病。病理检查发现肝内胆管迂曲扩张、发育异常。它可能与肝纤维化（格伦巴赫病）有关，也可能无关（卡罗利病）。常见的另一个发现是婴儿型多囊肾。本文报告3例病例，并讨论其放射学和超声检查结果。
