Houdee G, Beylot C, Doutre M S, Bioulac P, Bouchet H
Ann Dermatol Venereol. 1984;111(4):359-68.
A case of hemicorporeal cutis marmorata telangiectatica congenita is described. The ultrastructural study showed dilated capillaries with an increase of pericytes number. Some particular elements are discussed: --rare occurrence of hemi-corporeal distribution; --ultrastructural aspects with increased pericytes, previously observed; --frequency of associated abnormalities, cutaneous hemangiomas, varix, difference of length of the limbs, ...; --more frequently regressive evolution; --etiopathogeny, still uncertain, with capillaries abnormalities, perhaps dysembryoplasic and/or induced by neurovegetative disorder. Teratogenic factors (drug, chemical or others) has been suggested but not proved.
本文描述了一例先天性半身血管扩张性大理石样皮肤病例。超微结构研究显示毛细血管扩张，周细胞数量增加。讨论了一些特殊情况：——半身分布罕见；——先前观察到的周细胞增多的超微结构特征；——相关异常的发生率、皮肤血管瘤、静脉曲张、肢体长度差异等；——更常出现退行性演变；——病因仍不确定，存在毛细血管异常，可能是胚胎发育异常和/或由植物神经紊乱引起。已提出致畸因素（药物、化学物质或其他），但尚未得到证实。
