家族性持续性肺动脉高压
Familial persistent pulmonary hypertension.
作者信息
Shohet I, Reichman B, Schibi G, Brish M
出版信息
Arch Dis Child. 1984 Aug;59(8):783-5. doi: 10.1136/adc.59.8.783.
Abstract
We report three siblings who presented with a clinical picture of persistent pulmonary hypertension of newborn and died between 4 and 15 days of age. Pulmonary artery pressure in all was above systemic values, with a right to left shunt via either the foramen ovale or ductus arteriosus, or both. Histology of the pulmonary vascular bed showed extension of muscle into small arteries which are normally non-muscular.
摘要
我们报告了三名患有新生儿持续性肺动脉高压临床表现的兄弟姐妹，他们在4至15日龄之间死亡。所有人的肺动脉压力均高于体循环压力，存在通过卵圆孔或动脉导管或两者的右向左分流。肺血管床的组织学检查显示，肌肉延伸至通常无肌肉的小动脉。
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