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食管闭锁合并双瘘:漏诊的异常情况。

Esophageal atresia with double fistula: the missed anomaly.

作者信息

Johnson A M, Rodgers B M, Alford B, Minor G R, Shaw A

出版信息

Ann Thorac Surg. 1984 Sep;38(3):195-200. doi: 10.1016/s0003-4975(10)62236-9.

DOI:10.1016/s0003-4975(10)62236-9
PMID:6476941
Abstract

Of the various anatomical types of atresia, that of esophageal atresia and double fistula is said to be the least common. In most series, frequency is less than 1%. Seventy-eight patients with esophageal atresia were treated at the University of Virginia Medical Center between 1955 and 1983. Six of them had esophageal atresia and double fistula, and in 5 of these 6, this anomaly was not diagnosed preoperatively and was not detected intraoperatively. Our experience suggests that proximal "pouchograms" are essential in the preoperative evaluation of these patients to detect the presence of esophageal atresia and double fistula. The morbidity and mortality occasioned by overlooking this anomaly far exceed the risk of the contrast study.

摘要

在各种闭锁的解剖类型中,食管闭锁合并双瘘据说最为少见。在大多数病例系列中,其发生率低于1%。1955年至1983年间,弗吉尼亚大学医学中心共治疗了78例食管闭锁患者。其中6例为食管闭锁合并双瘘,在这6例中的5例,术前未诊断出这种异常,术中也未检测到。我们的经验表明,近端“袋状造影”对于这些患者术前评估以检测食管闭锁合并双瘘的存在至关重要。忽视这种异常所导致的发病率和死亡率远远超过造影检查的风险。

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Esophageal atresia with double fistula: the missed anomaly.食管闭锁合并双瘘:漏诊的异常情况。
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The combination of pure oesophageal atresia with an associated missed H-type tracheo-oesophageal fistula.单纯食管闭锁合并漏诊的H型气管食管瘘。
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Near-missed upper tracheoesophageal fistula in esophageal atresia.食管闭锁中近漏诊的上气管食管瘘
Eur J Pediatr. 2009 Oct;168(10):1281-4. doi: 10.1007/s00431-009-0926-z. Epub 2009 Feb 5.