Makhmudov M M, Alekian B G
Kardiologiia. 1984 Jul;24(7):41-5.
Although Ebstein's anomaly occurs mostly in isolation, in 2 to 5% of cases it is combined with pulmonary artery stenosis. This combination noticeably aggravates the natural course of the disease and complicates the diagnosis of the pathology. On the basis of five observations the authors present the specific differential-diagnostic signs which help to make the correct diagnosis. The key role in the identification of combined forms of Ebstein's anomaly is played by the catheterization of the cardiac chambers and by angiocardiography.
虽然埃布斯坦畸形大多单独出现,但在2%至5%的病例中,它与肺动脉狭窄合并存在。这种合并明显加重了疾病的自然病程,并使病理诊断复杂化。基于五项观察结果,作者提出了有助于做出正确诊断的特定鉴别诊断体征。心腔导管检查和心血管造影在识别埃布斯坦畸形合并形式中起着关键作用。