[Extreme Ebstein's anomaly].

The incidence of Ebstein's anomaly among patients with congenital heart disease is about 0.5 and 1% among autopsy cases. Among 279 autopsy cases with congenital heart disease of the period from 1978 to 1982 we found 3 Ebstein's anomalies. The reported case is a rare combination of Ebstein's anomaly with ventricular L-loop, corrected transposition of the great arteries, atresia of aortic valve, hypoplasia of the aorta and of the aortic arch, coarctation of the aorta and septum secundum defect. Such a case has not been communicated in the literature. The case is described and the embryological development of the abnormalities is discussed.