Angelini P, Leachman R D
G Ital Cardiol. 1978;8(4):417-31.
After formulating the definition of double outlet right ventricle (DORV) as the persistence origin of the trunco-conal structures from the right ventricle, 64 autopsy cases meeting this definition were reviewed. A wide spectrum of anatomic variations of DORV were found. A classification is proposed based upon the type of relationship between the great vessels and upon the presence and type of ventricular septal defect. Twenty-five cases had normally crossed great arteries (13 of which had pulmonic stenosis), nine cases had transposed vessels and 23 cases had a double muscular conus and a side-by-side arrangement of the great vessels in the frontal view, a relationship called "partial distortion" or atypical transposition. Seven cases had absent trunco-conal septum (common truncus). Only one case had intact ventricular septum. Anterior ventricular septal defect was found only in cases with partial distortion or common truncus. Angiographic and surgical correlations are presented. Because of their great heterogeneity, the need for detailed description of the anatomy of the individual case of DORV is emphasized.
在将双出口右心室（DORV）定义为动脉圆锥结构持续起源于右心室之后，回顾了64例符合该定义的尸检病例。发现了DORV广泛的解剖变异。基于大血管之间的关系类型以及室间隔缺损的存在和类型提出了一种分类方法。25例有正常交叉的大动脉（其中13例有肺动脉狭窄），9例有血管转位，23例有双肌性圆锥且在额面观大血管呈并列排列，这种关系称为“部分扭曲”或非典型转位。7例无动脉圆锥间隔（共同动脉干）。仅1例室间隔完整。前位室间隔缺损仅在部分扭曲或共同动脉干的病例中发现。展示了血管造影和手术相关性。由于其高度异质性，强调了对DORV个体病例解剖结构进行详细描述的必要性。
