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先天性大理石样皮肤血管扩张症:一例报告

Cutis marmorata telangiectatica congenita: a case report.

作者信息

Altman A R, Tschen J A, Wolf J E

出版信息

Pediatr Dermatol. 1984 Jan;1(3):223-5. doi: 10.1111/j.1525-1470.1984.tb01121.x.

Abstract

Cutis marmorata telangiectatica congenita (CMTC) is a rare cutaneous vascular disorder that was first described in 1922 by Van Lohuizen (1). The clinical presentation is one of persistent cutis marmorata, phlebectasia, telangiectasia, and areas of ulcerations. The disorder shows slow clinical improvement over time. Previously, CMTC has also been described as congenital generalized phlebectasia (2-7), congenital phlebectasia (8), nevus vascularis reticularis (9), congenital livedo reticularis (10), and livedo telangiectatica (11). The following is a case report.

摘要

先天性大理石样皮肤血管扩张症(CMTC)是一种罕见的皮肤血管疾病,于1922年由范·洛胡伊曾首次描述(1)。临床表现为持续性大理石样皮肤、静脉扩张、毛细血管扩张和溃疡区域。随着时间的推移,该疾病在临床上显示出缓慢的改善。以前,CMTC也被描述为先天性全身性静脉扩张(2 - 7)、先天性静脉扩张(8)、网状血管痣(9)、先天性网状青斑(10)和毛细血管扩张性青斑(11)。以下是一例病例报告。

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