Kalus R, Lavey E B
Ann Plast Surg. 1984 Sep;13(3):230-3. doi: 10.1097/00000637-198409000-00010.
A severe case is reported of a rare skin disorder characterized by multiple intracutaneous cystic lesions; the condition is difficult to manage and impossible to cure. The complicating cystic infections that accompany the condition are treated acutely using sound surgical principles, yet long-term management remains a difficult and unsolved problem. Some of the approaches to treatment are discussed. Surgical cures are usually precluded by the extensive nature of the disease. Perhaps most disheartening is the devastating social and psychological damage resulting from the progressive facial and bodily disfigurement, for which there is at present no satisfactory treatment.
报告了一例严重的罕见皮肤疾病,其特征为多个皮内囊性病变;这种病症难以处理且无法治愈。伴随该病症的并发囊性感染采用合理的外科原则进行急性治疗,但长期管理仍然是一个困难且未解决的问题。文中讨论了一些治疗方法。由于疾病的广泛性,通常无法通过手术治愈。或许最令人沮丧的是,面部和身体的渐进性毁容造成了严重的社会和心理损害,目前对此尚无令人满意的治疗方法。