Kingsley D, Till K, Hoare R
J Neurol Neurosurg Psychiatry. 1978 Apr;41(4):312-8. doi: 10.1136/jnnp.41.4.312.
Tne cases of growing fractures seen in the last 10 years are presented. Six of the patients sustained their injury within the first six months of life. The defects formed rapidly, several within two or three months after injury. There was enlargement of the defect in only one case after the date of discovery. Although the defects involved the parietal bone most commonly, in four out of 10 the lesion crossed either the coronal or the lambdoid suture. The edges of the defects were usually thickened; in some areas they were saucer-shaped but in two cases there was erosion of the outer table of the skull at a distance from the margin of the defect, the erosion being related to an extracranial fluid-filled cavity in continuity with a porencephalic cyst. The ipsilateral ventricle was usually dilated and in a number of cases was associated with a porencephalic cyst. In no case was a "leptomeningeal cyst" found beneath the defect at operation. A detailed review confirms many of the findings previously described but suggests that the pathology of the condition is still not fully understood. Computed tomography, undertaken in one case, appears to be the examination of choice. Further light may be thrown on the pathogenesis of this condition by the use of intracystic, intrathecal, and intraventricular water-soluble contrast media.
本文报告了过去10年中所见的生长性骨折病例。6例患者在出生后的前6个月内受伤。缺损形成迅速,数例在受伤后两三个月内形成。发现后仅1例缺损有扩大。虽然缺损最常累及顶骨,但10例中有4例病变跨越冠状缝或人字缝。缺损边缘通常增厚;有些区域呈碟形,但有2例在距缺损边缘一定距离处颅骨外板有侵蚀,这种侵蚀与一个与脑穿通性囊肿相连的颅外液性腔有关。同侧脑室通常扩张,许多病例伴有脑穿通性囊肿。手术时在缺损下方均未发现“软脑膜囊肿”。详细回顾证实了许多先前描述的发现,但表明该病的病理仍未完全明了。1例患者进行的计算机断层扫描似乎是首选检查。通过使用囊内、鞘内和脑室内水溶性造影剂,可能会进一步阐明该病的发病机制。