Björck S, Johansson S L, Aurell M
Scand J Urol Nephrol. 1984;18(4):343-6. doi: 10.3109/00365598409180208.
A 45-year-old man who presented with acute renal insufficiency is described. He deteriorated during haemodialysis, developed severe gastrointestinal bleedings, and died two months after his initial admission. Histopathological changes responsible for his renal disease were focal narrowing and occlusion of the arteries of the kidneys due to concentric intimal proliferation. These findings are consistent with those described in Köhlmeier-Degos' disease, a fatal cutaneo-intestinal arterio-occlusive syndrome. Therefore we consider our patient to represent a case of this disease, which may be added to the list of rare causes of acute renal failure.
本文描述了一名45岁的急性肾功能不全男性患者。他在血液透析过程中病情恶化，出现严重的胃肠道出血，并在初次入院两个月后死亡。导致其肾脏疾病的组织病理学变化是由于同心性内膜增生导致肾动脉局灶性狭窄和闭塞。这些发现与Köhlmeier-Degos病（一种致命的皮肤-肠道动脉闭塞综合征）中描述的情况一致。因此，我们认为该患者代表了这种疾病的一个病例，这种疾病可能会被添加到急性肾衰竭的罕见病因列表中。
