Meline N C, Fox R L
J Aud Res. 1984 Jul;24(3):175-82.
Palatal myoclonus, the rapid rhythmic contraction of palatal muscles, is a rare neurological disorder with many etiologies. Although most disease processes associated with this disorder affect the cerebellum, the auditory symptoms are often the first clue to diagnosis. Existing literature was reviewed in terms of auditory symptoms, pathophysiology, audiologic diagnostic procedures and rehabilitative strategies. In addition, a case study of a 34-yr-old woman who has had this highly peculiar degenerative disorder for over 20 yrs was described. Implications for appropriate rehabilitation strategies were addressed and the importance of comprehensive management was stressed.
腭肌阵挛是腭部肌肉快速有节律的收缩,是一种病因多样的罕见神经系统疾病。尽管与该疾病相关的大多数病理过程会影响小脑,但听觉症状往往是诊断的首要线索。本文就听觉症状、病理生理学、听力学诊断程序及康复策略对现有文献进行了综述。此外,还描述了一名34岁女性的病例研究,该女性患有这种极其特殊的退行性疾病已超过20年。文中探讨了合适康复策略的意义,并强调了综合管理的重要性。