Minami M, Machida K, Nishikawa J, Iio M
Radiat Med. 1984 Jan-Mar;2(1):49-55.
Maffucci syndrome is a congenital, non-hereditary mesodermal dysplasia associated with multiple enchondromas and hemangiomas. The high risk of development of malignant tumors is well-known. A case of Maffucci syndrome in a 68-year-old man who suffered from multiple malignant degeneration and who was given a bone scintigraphic examination is reported with radiological and pathological findings. The scintigraphic findings are different for two histological different chondrosarcomatous lesions. It seems that uptake of Tc-99m MDP increases with the degree of calcification rather than whether the lesion is benign or malignant.
马富西综合征是一种先天性、非遗传性的中胚层发育异常，与多发性内生软骨瘤和血管瘤相关。众所周知，其发生恶性肿瘤的风险很高。本文报告了一例68岁男性马富西综合征患者，该患者发生了多处恶性病变，并接受了骨闪烁显像检查，同时给出了影像学和病理学结果。对于两种组织学不同的软骨肉瘤病变，闪烁显像结果有所不同。似乎锝-99m亚甲基二膦酸盐（Tc-99m MDP）的摄取随着钙化程度的增加而增加，而不是取决于病变是良性还是恶性。
