Lilja P, Evander A, Ihse I
Acta Chir Scand. 1978;144(1):35-7.
Two Swedish kindreds with hereditary pancreatitis are reported. The onset of symptoms was in early childhood. Otherwise the clinical course did not differ from the non-hereditary form. In no patients were found signs of alcohol-overconsumption, hyperparathyreoidism, hyperlipidemia or mucoviscoidosis. Three patients with intractable pain and frequent hospitalization were operated on with pancreatico-jejunostomy as described by Puestow-Gillesby, with excellent results. Although the observation periods are short (0.5, 2 and 4 years, respectively) it seems legitimate to recommend the operation also for the hereditary form of pancreatitis if intractable pain or frequent exacerbations are present.
本文报道了两个患有遗传性胰腺炎的瑞典家族。症状始于儿童早期。除此之外，临床病程与非遗传性形式并无差异。未在任何患者中发现酒精过度摄入、甲状旁腺功能亢进、高脂血症或黏液黏稠病的迹象。三名患有顽固性疼痛且频繁住院的患者接受了如普斯托-吉莱斯比所描述的胰空肠吻合术，效果极佳。尽管观察期较短（分别为0.5年、2年和4年），但如果存在顽固性疼痛或频繁发作，对于遗传性胰腺炎推荐进行该手术似乎是合理的。
