Hiersche H D, Wagner R
Geburtshilfe Frauenheilkd. 1983 Apr;43(4):250-2. doi: 10.1055/s-2008-1037100.
We report a case of incomplete testicular feminisation in a 53 years old, third time married patient. Prominent symptoms were a slightly masculine structure of the body, masculine features and a hypertrophy of the clitoris. The reason for hospitalization was a lower abdominal tumour. Histologically it was a hydrocele with a testicle including a Leydig's cell-tumour without any signs of malignancy. On the opposite side was on atrophic testicle without spermiogenesis too. As usual the syndrome of incomplete testicular feminisation was discovered very late. Therefore, the necessary psychological guidance, especially from the beginning of puberty and the oncological control to exclude a tumour of the testicle had been left undone. It is the purpose of this report to draw attention to the aspect of this disease despite its rare occurrence in a ratio of 1:2,000 to 1:20,000.
我们报告一例53岁、第三次结婚的患者的不完全性睾丸女性化病例。突出症状为身体结构略显男性化、具有男性特征以及阴蒂肥大。住院原因是下腹部肿瘤。组织学检查显示为伴有睾丸的鞘膜积液,其中睾丸包含一个无任何恶性迹象的莱迪希细胞瘤。另一侧是一个萎缩的睾丸,也无精子发生。与往常一样,不完全性睾丸女性化综合征发现得非常晚。因此,必要的心理指导,尤其是从青春期开始以及肿瘤学检查以排除睾丸肿瘤,都没有进行。尽管这种疾病的发病率很低,为1:2000至1:20000,但本报告的目的是提请注意该疾病的这一方面。