Lucas M, Serrano V, Naval L, Balda I
Rev Stomatol Chir Maxillofac. 1984;85(2):119-22.
This study describes four cases of Paget's deforming dystrophy involving the jaw. In three of them the course of the disease affected only the bone involved whilst in the fourth the bones of the vault of the skull and some cranial nerves were affected in time. The prevalence of the female sex and of involvement of the maxilla was evident. The mandible was involved in only one case. Biochemical abnormalities were the same in all cases as well as being identical to those in cases of Paget's disease with multiple bone involvement. The authors suggest medical treatment (calcitonin, Na etidronate, mitramycin ) and surgery only when required for bone remodelling when there is interference with function.
本研究描述了4例累及颌骨的佩吉特畸形性骨营养不良病例。其中3例疾病过程仅累及受累骨骼，而第4例患者颅骨穹窿骨和一些颅神经最终也受到影响。女性患病率以及上颌骨受累情况较为明显。仅1例累及下颌骨。所有病例的生化异常情况相同，且与多骨受累的佩吉特病病例相同。作者建议进行药物治疗（降钙素、依替膦酸钠、光辉霉素），仅在功能受到影响需要进行骨重塑时才进行手术。
