PiZ型肺气肿气流阻塞的自然史。美国国立心肺血液研究所研讨会报告。 - Suppr

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The natural history of air-flow obstruction in PiZ emphysema. Report of an NHLBI workshop.

作者信息

Buist A S, Burrows B, Eriksson S, Mittman C, Wu M

出版信息

Am Rev Respir Dis. 1983 Feb;127(2):S43-5. doi: 10.1164/arrd.1983.127.2P2.S43.

DOI:10.1164/arrd.1983.127.2P2.S43

PMID:6600892

Abstract

摘要

相似文献

The natural history of air-flow obstruction in PiZ emphysema. Report of an NHLBI workshop.PiZ型肺气肿气流阻塞的自然史。美国国立心肺血液研究所研讨会报告。

Am Rev Respir Dis. 1983 Feb;127(2):S43-5. doi: 10.1164/arrd.1983.127.2P2.S43.

Normal diffusing capacity in patients with PiZ alpha(1)-antitrypsin deficiency, severe airflow obstruction, and significant radiographic emphysema.伴有PiZα1-抗胰蛋白酶缺乏、严重气流阻塞和显著影像学肺气肿的患者的弥散能力正常。

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[The variability of clinical presentation of chronic obstructive pulmonary disease in patients with hereditary alpha-1 antitrypsin deficiency].[遗传性α-1抗胰蛋白酶缺乏症患者慢性阻塞性肺疾病的临床表现变异性]

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A matched-pair study of the leukocyte elastase-like activity in normal persons and in emphysematous patients with and without alpha 1-antitrypsin deficiency.一项针对正常人以及患有和未患有α1抗胰蛋白酶缺乏症的肺气肿患者白细胞弹性蛋白酶样活性的配对研究。

Am Rev Respir Dis. 1980 Feb;121(2):253-61. doi: 10.1164/arrd.1980.121.2.253.

[Alpha 1-antitrypsin deficiency and emphysema. Replacement therapy?].[α1-抗胰蛋白酶缺乏症与肺气肿。替代疗法？]

Tidsskr Nor Laegeforen. 1989 Aug 10;109(22):2142-5.

[Long-term follow-up and autopsy of a Japanese patient who had emphysema associated with alpha 1-antitrypsin deficiency].

Nihon Kyobu Shikkan Gakkai Zasshi. 1996 Sep;34(9):1040-3.

Assessment of alpha-1-antitrypsin deficiency heterozygosity as a risk factor in the etiology of emphysema. Physiological comparison of adult normal and heterozygous protease inhibitor phenotype subjects from a random population.评估α-1抗胰蛋白酶缺乏杂合性作为肺气肿病因中的一个风险因素。对来自随机人群的成年正常和杂合蛋白酶抑制剂表型受试者进行生理比较。

J Clin Invest. 1979 Feb;63(2):299-309. doi: 10.1172/JCI109303.

Collaborative study to assess risk of lung disease in Pi MZ phenotype subjects.评估Pi MZ表型受试者肺部疾病风险的合作研究。

Am Rev Respir Dis. 1984 Sep;130(3):386-90. doi: 10.1164/arrd.1984.130.3.386.

Coagulation-fibrinolytic inhibitors on familial cases of alpha 1-antitrypsin deficiency.α1抗胰蛋白酶缺乏症家族病例中的凝血-纤维蛋白溶解抑制剂

Nihon Ketsueki Gakkai Zasshi. 1982 Jul;45(4):800-5.

[Pulmonary emphysema and hepatic involvement by alpha-1 antitrypsin deficiency in two adults with a PiZ phenotype (author's transl)].两名具有PiZ表型的成年人的α-1抗胰蛋白酶缺乏症所致肺气肿和肝脏受累（作者译）

Nouv Presse Med. 1978 Apr 8;7(14):1191-4.

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Validation of computed tomographic lung densitometry for monitoring emphysema in alpha1-antitrypsin deficiency.计算机断层扫描肺密度测定法用于监测α1抗胰蛋白酶缺乏症患者肺气肿的验证

Thorax. 2006 Jun;61(6):485-90. doi: 10.1136/thx.2005.054890. Epub 2006 Mar 14.

Alpha-1 antitrypsin deficiency is not a rare disease but a disease that is rarely diagnosed.α-1抗胰蛋白酶缺乏症并非罕见疾病，而是一种很少被诊断出来的疾病。

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Pulmonary function in children with homozygous alpha1-protease inhibitor deficiency.

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Thorax. 1994 Jul;49(7):695-8. doi: 10.1136/thx.49.7.695.

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