Congenital lobar emphysema with tracheal bronchus.

A three-month-old infant presenting with a heart murmur and respiratory distress was found to have a Tetralogy of Fallot, a right aortic arch, and a hyperaerated right upper lobe of lung. Bronchoscopy and bronchography revealed that the bronchus to the emphysematous lobe arose from the distal trachea. No similar patient has been reported to my knowledge.