Lipoamide dehydrogenase in cultured human skin fibroblasts.
作者信息
Melançon S B, Dallaire L, Potier M
出版信息
Clin Chim Acta. 1978 Jul 1;87(1):29-34. doi: 10.1016/0009-8981(78)90053-0.
PMID:668142
Abstract
Lipoamide dehydrogenase was identified in cultured skin fibroblasts of normal individuals and patients with Friedreich's ataxia. The optimum conditions for its assay were defined. Data disclosed a normal range of 36--122 mumol/min/mg protein in control fibroblasts and 61--112 mumol/min/mg protein in patients fibroblasts. Numerous precautions should be taken in handling fibroblast cultures for lipoamide dehydrogenase determination.
摘要
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