Label L S, Tandan R, Albers J W
Neurology. 1983 Jul;33(7):936-9. doi: 10.1212/wnl.33.7.936.
A 25-year-old man with the skin lesions of malignant atrophic papulosis had clinical and electrodiagnostic evidence of a multifocal asymmetric myelomalacia or polyradiculopathy in association with elevated CSF protein and hypoglycorrhachia. Autopsy findings included widespread infarctions and necrosis of brain, brainstem, and spinal cord. The combined clinical and laboratory findings were similar to those seen in systemic lupus erythematosus, sarcoidosis, or meningeal carcinomatosis. Thus, malignant atrophic papulosis should be added to the differential diagnosis of either polyradiculopathy or myelomalacia.
一名患有恶性萎缩性丘疹病皮肤损害的25岁男性，有临床和电诊断证据表明存在多灶性不对称性脊髓软化或多发性神经根病，同时伴有脑脊液蛋白升高和脑脊液低糖。尸检结果包括脑、脑干和脊髓广泛梗死和坏死。临床和实验室综合检查结果与系统性红斑狼疮、结节病或脑膜癌病所见相似。因此，恶性萎缩性丘疹病应列入多发性神经根病或脊髓软化的鉴别诊断之中。
